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The phrase "is extremely rare" is perfectly acceptable and commonly used in written English.
You can use it to describe a situation when something happens very rarely, or is in short supply. For example, "A snowstorm in this region is extremely rare."
Dictionary
is extremely rare
adverb
To an extreme degree
synonyms
Exact(57)
The disease is extremely rare.
SNAP fraud is extremely rare.
True colorblindness is extremely rare.
But application in Europe is extremely rare.
An unblemished career record is extremely rare.
Polonium is extremely rare in nature.
Primarily an animal illness, it is extremely rare in humans.
Pilgrim Century silver, from the 17th century, is extremely rare.
Violence against army soldiers is extremely rare in China.
This universal artistic quality is "extremely rare", Pevear says.
"Load testing of a new design is extremely rare.
More suggestions(16)
is extremely strange
is extremely sparse
is tremendously rare
is extremely frequent
is extremely precious
is highly rare
is extremely thin
is extremely infrequent
is extremely unique
is exceptionally rare
is extremely neat
is extremely unresponsive
is extremely painful
is extremely exciting
is extremely counterproductive
is extremely dangerous
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Since I tried Ludwig back in 2017, I have been constantly using it in both editing and translation. Ever since, I suggest it to my translators at ProSciEditing.

Justyna Jupowicz-Kozak
CEO of Professional Science Editing for Scientists @ prosciediting.com